The importance of adequate bronchiectasis treatment

Abstract

Kartagener syndrome is a rare autosomal recessive genetic disease, progressive damage to the respiratory system and situs inversus. Although patients with Kartagener syndrome management remains unclear, and the evidence is limited, but it is important to follow up these patients, appropriate and common supervisory framework to prevent future lung damage. In this case report, we announce a 25 year old woman with a diagnosis of Kartagener syndrome, committed 14 years ago. In 2015, patient was tested for cystic fibrosis and delF508 mutation in heterozygous state was found. The patient was under the supervision of the various areas of the respiratory clinic doctors. Daily physiotherapy, long-acting bronchodilators and appropriate antibiotic treatment has been used for treatment. After 7 years of treatment we have a good treatment results for lung function and radiological data is stable.